Pulmonary Atresia with Ventricular Septal Defect and Multiple Aortopulmonary Collaterals

Pulmonary atresia with ventricular septal defect (PA/VSD) and multiple aortopulmonary collaterals (MAPCAs) is a rare and complex congenital heart defect that disrupts normal blood flow to the lungs. The pulmonary trunk is atretic, with confluent branches supplying only certain lung segments, and compensatory circulation occurs through collateral vessels. Four aortopulmonary collaterals are typically present, with two connecting to the pulmonary artery branches and the other two supplying lung segments independently. These abnormalities lead to significant anatomical and clinical challenges, as the spatial relationships between the collaterals, the tracheobronchial tree, and the pulmonary trunk's position relative to the right ventricular outflow tract are critical to the defect's management. This condition results in cyanosis and requires surgical intervention to reconstruct pulmonary circulation.

The model is composed of eight .STL files corresponding to each anatomical structure – aorta, four files for major aortopulmonary collateral arteries (MAPCA), right and left pulmonary arteries (RVA an LVA), right ventricular outflow tract (RVOT) and trachea. When combined together, they provide a general anatomical structure of the child heart as presented at the figure below:

The models are small (between 354 kB up to 8,2 MB). Printing each structure is suitable even for smaller 3D printers. We do recommend to print each structure by different color and then glue it together to make a nice looking model.